Rhabdomyosarcoma is a malignant neoplasm derived from striated muscle cells. It is relatively common in the paediatric population and often occurs in the head and neck region. In the adult population, rhabdomyosarcoma usually presents in the limbs and it is extremely rare for this disease to occur in the head and neck. We present the case of an 18 year old male who presented to our ENT department with an aural polyp. Histopathological examination of the lesion confirmed a diagnosis of rhabdomyosarcoma. This case highlights the need for a high level of clinical suspicion and early biopsy of aural polyps to exclude neoplastic conditions.