Objective: The authors present a rare case of paediatric sphenoidal mucopyocele mimicking a tumour.
Methods: A case report and literature review of sphenoid mucoceles in the paediatric population.
Results: The authors present a case of sphenoidal mucopyocele in childhood initially thought to be a rhabdomyosarcoma. We discuss the presentation, investigation and surgical management of this rare entity. We also provide radiological evidence of this pathology.
Conclusion: Paranasal sinus mucoceles are uncommon in the paediatric population; with sphenoidal mucoceles being extremely rare. Endoscopic endonasal surgery is nowadays the gold standard for treating sphenoid mucoceles.